ASPS in an unusual sites - heart, bladder, retroperitoneum

[Olga]

A few of the new articles are describing ASPS in a number of unusual sites:

1. Alveolar Soft-part Sarcoma of the Urinary Bladder With Urethral Recurrence: A Unique Case With Emphasis on Differential Diagnoses and Diagnostic Utility of an Immunohistochemical Panel Including TFE3.
American Journal of Surgical Pathology. 30(10):1322-1325, October 2006
http://www.ajsp.com/pt/re/ajsp/abstract ... 45!8091!-1
They report a unique case of ASPS presenting in the bladder with subsequent urethral recurrence in a 25-year-old woman.

2. Alveolar soft part sarcoma in brain with cardiac metastasis A case report.
International Journal of Cardiology , online, Letter to the Editor:
http://www.ncbi.nlm.nih.gov/entrez/quer ... med_docsum
From this abstract: "The use of modern treatment modalities, such as combination of surgery, and radiotherapy, may significantly prolong the survival time in many patients. Because of the long-term period with symptomatic brain tumors in this disease, the patients should be treated even in the presence of multiple metastases in other organs."
This is an important issue as some of our patients were not treated when disease was found metastatic at the presentation or progressed.

3. Alveolar soft-part sarcoma of the retroperitoneum.
International Journal of Urology, Volume 13, Number 10, October 2006, pp. 1355-1357(3)
http://www.ncbi.nlm.nih.gov/entrez/quer ... med_DocSum
Computed tomography showed a tumor (17 × 11 × 10 cm) in the left retroperitoneal space.