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Primary renal neoplasms with the ASPL-TFE3 gene fusion of ASPS
Posted: Sun Sep 11, 2016 9:01 am
by D.ap
Primary renal neoplasms with the ASPL-TFE3 gene fusion of alveolar soft part sarcoma: a distinctive tumor entity previously included among renal cell carcinomas of children and adolescents.
http://www.ncbi.nlm.nih.gov/m/pubmed/11438465/
Re: Primary renal neoplasms with the ASPL-TFE3 gene fusion of ASPS
Posted: Sun Sep 11, 2016 7:46 pm
by Olga
I think they now call it papillary RCC? We had a member of this board being misdiagnosed as having ASPS when in fact it was this one. It is a more aggressive faster growing cancer, but its pattern of metastasis resembles the one of ASPS. They both a re the members of the MiT Family Translocation cancers.
Re: Primary renal neoplasms with the ASPL-TFE3 gene fusion of ASPS
Posted: Mon Sep 12, 2016 5:21 am
by D.ap
Interesting Olga
Thank you for the added info
I couldn't tell whether they were saying it was now called primary asps of the kidney ?
When Josh was in Germany in 2013 he befriended a young man who was battling this cancer. Metastic lung tumors being removed after the kidney was treated .
This article will hopefully alert a new dx'd patient to get a second option to their diagnosis so as to make the right choice for treatment
Papillary , RCC needs a more aggressive and there is more of a sense of urgency in treatment as it progresses faster than ASPS